MARFAN SYNDROME
1. The most recognizable skeletal abnormality associated with Marfan syndrome (MFS) is
a. Kyphoscoliosis
b. Pectus excavatum
c. Arachnodactyly
d. Abnormal height
2. Eighty percent of MFS mortality is linked to
a. Aortic aneurysm and dissection
b. Pericardial tamponade
c. Myocardial infarction
d. Ruptured chordae tendineae
3. Best heard with the patient sitting and leaning forward, the characteristic murmur of MFS is
a. Medium to high pitched with prolonged apical impulse
b. High pitched blowing during early diastole
c. Low pitched with accentuated S1
d. Soft to loud associated with a thrill
4. Patients with MFS suffering from a spontaneous pneumothorax may present with
a. Acute shortness of breath
b. Pleuritic chest pain
c. Hemoptysis
d. Distant breath sounds
5. The standard of care in the treatment of patients who have MFS is
a. ACE inhibitors
b. Calcium channel blockers
c. Beta-blockers
d. Loop diuretics
6. Which medication has demonstrated its ability to arrest the development of many manifestations of MFS?
a. Interferon
b. Dexamethasone
c. Levodopa
d. Losartan
THE FEBRILE INFANT, PART 1
7. For evaluation purposes in the workup of the febrile infant, the neonate is defined as an infant from birth to age
a. 7 days
b. 14 days
c. 28 days
d. 35 days
8. Up to one-third of serious bacterial infections (SBIs) in young infants are
a. Urinary tract infections
b. Pneumonia
c. Bacterial gastroenteritis
d. Cellulitis
9. The predominant gram-negative enteric organism in infants with an SBI is
a. Klebsiella pneumoniae
b. Shigella species
c. Escherichia coli
d. Serratia marcescens
10. A low-risk criteria for SBI in the febrile infant is
a. <2,500 band cells/mm3 on CBC
b. Stool smear negative for blood
c. <50 WBCs/mm3 in CSF
d. No WBCs/hpf on urinalysis
11. Recommended empiric antibiotic therapy for infants younger than 29 days includes
a. Azithromycin
b. Tetracycline
c. Sulfamethoxasole
d. Ampicillin
12. Young infants managed as outpatients can be given a single IM injection of
a. Ciprofloxacin
b. Clindamycin
c. Ceftriaxone
d. Vancomycin